ListarGI- GRINCAR - Artigos por tema "Distrofia muscular de Emery-Dreifuss"
Mostrando ítems 1-1 de 1
-
Emery–Dreifuss muscular dystrophy Type 1 is associated with a high risk of malignant ventricular arrhythmias and end-stage heart failure
(Oxford Academic, 2023-08-28)[Abstract] Emery–Dreifuss muscular dystrophy (EDMD) is caused by variants in EMD (EDMD1) and LMNA (EDMD2). Cardiac conduction defects and atrial arrhythmia are common to both, but LMNA variants also cause end-stage heart ...